Solid and Papillary Cystic Neoplasm of Pancreas in Children

(1)

=Abstract=

Solid and Papillary Cystic Neoplasm of Pancreas in Children

Sung-II Choi, M.D., Soo-Myung Oh, M.D.

Department of Surgery, Kyung Hee University School of Medicine Seoul, Korea

Solid and papillary cystic neoplasm of pancreas is an uncommon low grade malignant tumor. It is predominant in young female between the second and third decades of life, and amenable to cure by surgical treatment. The authors report two cases of solid and papillary neoplasm of pancreas pathologically verified at Kyung Hee University Hospital. The first case was an ll-years old female patient and the other case was a 12-years old male. Symptoms were abdominal discomfort, nausea and vomiting in both cases and abdominal pain in the female patient. CT finding included a solid and papillary neoplasm of pancreas. The mass was well-demarcated with solid and cystic necrosis components. In the female patient, a large hematoma was found. Gross findings revealed apparent encapsulation, cystic degeneration and hemorrhagic necrosis.

Microscopically the tumors were characterized by distinctive solid and papillary patterns of cellular arrangement without local invasion. Both patients were discharged after surgery and followed up without any problem.

Index Words: Solid and papillary cystic neoplasm, Pancreas

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Correspondence: Soo-Myung Oh, M.D., Department oj Surgery, Kyung Hee University School of Medicine, Hoeki-dong, Dongdaemoon-gu, Seoul 130-702, Korea

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Fig. 1. Abdominal computerized tomogram of the case 1, showing heterogeneous low attenuation spherical mass in the pancreas tail without invasion.

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Fig. 2. Cross sectional view of the case 1, revealing a cystic solid mas measured 4.5 X4.5cm. Cut surface shows rather well encapsalated cystic and solid mass with necrosis and hemorrhage.

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Fig. 3. Microscopic findings of a solid and papillary epithelial neoplasm of the pancreas of the case 1 (H&E,

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Fig. 4. Abdominal

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fmding of the Case 2. A huge mass was composed with two portions with well encapsalation, one hemorrhage and the other hemorrhage and necrosis.

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Fig. 5. Gross fmding of the resected tumor (Case 2).

Encapsalated huge hemorrhagic cystic and solid mass in the pancreas tail is shown.

Fig. 6. Microscopic finding of the Case 2 (H&E, x 100), showing papillary epithelial growing. The papillary fibrovascular cores show characteristic perivascular hyalinizing and mixoid stroma.

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