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=Abstract=

:±O}.9-1Jrl-~lAl9-1 Henoch-Schonlein ~}l{!-~

Henoch-Schonlein Purpura in Pediatric Surgery

Dae Yeon Kim, M.D., Seong Chul Kim, M.D., In Koo Kim, M.D.

Division of Pediatric Surgery, Department of Surgery, University of Ulsan College of Medicine and Asan Medical Center

Seoul, Korea

Henoch-Schonlein purpura is a systemic vasculitis of unknown

etiology

that is probably related to an

autoimmune

phenomenon. Henoch-Schonlein purpura is characterized by a purpuric rash, arthralgia, nephritis, and

gastrointestinal

mani- festations. We reviewed 169

children

hospitalized

with a

diagnosis of Henoch- SchOnlein purpura between 1989

and

1998. One-hundred thirty-nine

(82.2 %)

had gastrointestinal findings including abdominal pain, nausea, vomiting and gas- trointestinal bleeding. Surgical consultations were obtained for ten children,

and

laparotomy was performed in five. Three children suspected of having appendi- citis underwent appendectomy

.

None had

appendicitis.

One child thought to have been intestinal

strangulation

was found to have hemorrhagic

edema

of the proximal jejunum and of the distal ileum. Another child underwent resection for an hemorrhagic infarct of the distal ileum. A high index of suspicion of this

disease

entity in the differential diagnosis of

abdominal

pain in children can avoid

unnecessary laparotomy

in most cases. However, life-threatening gastro- intestinal complications may occur in low percentage of cases. Prompt recognition and adequate radiologic

evaluation

of the abdominal manifestation of this

entity

is necessary for

early surgical

intervention.

Index Words:

Henoch-Scho-nlein purpura, Pediatric

sur~ery

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Correspondence: In Koo Kim, M.D., Division of Pedi- atric Surgery, Department of Surgery, University of Ulsan College of Medicine and Asan Medical Center, 388-1 PunRl1ap-donR, SonRpa-Ru, Seoul 138-736, Korea

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* N/V ; nausea/vomiting

UGI bleeding

Fig. 1. Clinical manifestations in 165 cases of Hen- och-Schonle!n purpura.

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GI $X Arthralgia Hematuria Proteinuria

* GI sx; gastrointestinal symptoms and signs

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Fig. 2. Clinical and laboratory findings in patients with Henoch-Schonlein purpura.

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Table 1. Criteria for the Classification of Henoch-Schonlein Purpura5 Criteria

1. Palpable purpura

2. Age";;20 at disease onset 3. Bowel angina

4. Wall granulocytes on biopsy

Definition

Slightly raised "palpable" hemorrhagic skin lesions. not related to thrombocytopenia.

Patient 20 years or younger at onset of first symptoms.

Diffuse abdominal pain. worse after meals. or the diagnosis of bowel ischemia. usually including bloody diarrhea.

Histologic changes showing granulocytes in the walls of arterioles or venules.

* The four criteria identified. two of which are necessary to make the diagnosis.

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£)-Y-1=- 7cl-!f-:::: 81.8 %0]9:1.2, A}~~O] ~~<o}7]

~ OJ] *~o] ~ i5~ "6}~ g 7cl-!f-1=- 44.3 % 0]9:1. q . He- noch-Schtinlein A}~~ ~.A}OJ]A1 'Ti'% A] i;~"6}~

(5)

t;j oj]-C- 5oj](3.0 %)~Jl, .J ~ ~71]'£ Q]:i!l-~~5'- 9.10]SU-C- '1l~0] SU9it;j 7cH--c- loj](0.6%)~c}.

Henoch-Schbnlein 7-}\1~..g. ~~ 7-}~ :7.]% 2]-11 (self-limited process)9.1 'iJ.AJ 7cl2}~ ~ 0 ]7-]~, 7-}

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~lj-o] '1:J7-] ~q. Henoch-Schonlein 7-}\1%o1]Al g.Aj 7H*~g ~0]7] ~tHA1-c- 0] ~~9.1 'iJ.AJ 7cl:i!]-9} ~~ g

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~J.~E-5'- i'-9.1 ~..g. 'iJ .AJ'tl-%JJl- ~-¥- 3':%:rrJ-7,:j A} %9.1 llJA}~ 7,:jA}5'- {}~j)}Jl 11~~ ~1i'g tHo]: ~q.

1. Stewart M, Savage JM, Bell B, McCord B:

Long term renal prognosis of Henoch-Schon- lein purpura in an unselected childhood popul- ation. Eur J Pediatr 147(2): 113-115, 1988 2. Tizard EJ: Henoch-Schonlein purpura. Arch

Dis Child 80: 380-383, 1999

3. Farley TA, Gillespie S, Rasoulpour M, Tolen- tino N, Hadler JL, Hurwitz E: Epidemiology of a cluster of Henoch-Schbnlein purpura. Am J Dis Child 143(7): 798-803, 1989

4. Cull DL, Rosario V, Lally KP, Ratner I, Ma- hour GH: Surgical implications of Henoch- Schonlein purpura. J Pediatr Surg 25(7):741- 743, 1990

5. Mills JA, Michel BA, Bloch DA, Calabrese LH, Hunder GG, Arend WP, Edworthy SM, Fauci AS, Leavitt RY, Lie JT, Lightfoot RW, Jr Masi AT, Mcshane DJ, Srevens MB, Wallace SL, Zvaifler NJ: The American Coll- ege of Rheumatology 1990 criteria for the classification of Henoch-Schbnlein purpura. Art- hr Rheumatol 33(8):1114-1121, 1990

6. Lindenauer SM, Tank ES: Surgical aspects of Henoch-Schonlein's purpura. Surgery 59:982- 987, 1966

7. Rosenblum ND, Winter HS: Steroid effects on the course of abdominal pain in children

with Henoch-Schbnlein purpura. Pediatrics 79 (6):1018-1021, 1987

8. Katz S, Borst M, Seekri J, Grosfeld JL: Sur- gical evaluation of Henoch-Schonlein purpura.

Experience with 110 children. Arch Surg 126 (7):849-854, 1991

9. ~

"'HI,

70 0]

T,

~ ~ {i:

7.J7iJ

~ 0] w'1l.'@

Henoch-Schbnlein 7-} \1~ loj]. qj ~

91

JJl-~ ~

7-] 48(3), 1995

10. Park SH, Kim CJ, Chi IG, Seo IK, Park KW: Gastrointestinal manifestations of Henoch -Schbnlein purpura. J Korean Med Sci 5(2):

101-104, 1990

11. Martinez-Frontanilla LA, Haase GM, Ernster JA, Bailey WC: Surgical complications in He- noch-Schonlein Purpura. J Pediatr Surg 19(4):

434-436, 1984

12. Glasier CM, Siegel MJ, McAlister WH, Shac- kelford GD: Henoch-Schonlein syndrome in children: gastrointestinal manifestations. AJR

136(6):1081-1085, 1981

13. Couture A, Veyrac C, Baud C, Galifer RB, Armelin I: Evaluation of abdominal pain in Henoch-Schbnlein syndrome by high frequency ultrasound. Pediatr Radiol 22(1):12-17, 1992 14. Hu SC, Feeney MS, McNicholas M, O'Halpin

D, Fitzgerald RJ: Ultrasonography to diagnose and exclude intussusception in Henoch-Schonl- ein purpura. Arch Dis Child 66(9): 1065-1 067,

1991

15. Tomomasa T, Hsu JY, Itoh K, Kuroume T:

Endoscopic findings in pediatric patients with Henoch-Schbnlein purpura and gastrointestinal symptoms. J Pediatr Gastroenterol Nutr 6(5):

725-729, 1987

16. Clark WR, Kramer SA: Henoch-Schbnlein purpura and the acute scrotum. J Pediatr Surg 21(11):991-992, 1986

17. 11 Aj~, 3'::,Aj

%,

~:7.] ~, :7.Pj~, 3':: '1l

T,

<j-

7.J~: if,Aj *~o] <it;~.'@ o}q~Et°J= 7-}\1

~ 01] qj ~ 'iJ .AJ.3j 2%. ~ o}:i!]- 36(8): 1124- 1131, 1993

18. Mohammed R: Acute appendicitis; a compli- cation of Henoch-Schbnlein purpura. J R Coli Surg Edinb 27(6):367, 1982

수치

Table  1.  Criteria  for  the  Classification  of Henoch- Schonlein  Purpura 5  Criteria

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